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Leiomyosarcoma of the main bronchus in a girl: A long‐time survivor with multiple lung metastases
Author(s) -
Takeda Fumihiro,
Yamagiwa Iwao,
Ohizumi Hiroyuki,
Shiono Satoshi
Publication year - 2004
Publication title -
pediatric pulmonology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.866
H-Index - 106
eISSN - 1099-0496
pISSN - 8755-6863
DOI - 10.1002/ppul.10456
Subject(s) - medicine , leiomyosarcoma , malignancy , left main bronchus , lung , bronchus , surgery , right main bronchus , respiratory disease , bronchoscopy , radiology
Primary leiomyosarcoma of the respiratory tract is a very rare malignancy, especially in childhood, with only 15 cases in patients under 16 years old having been reported. In the present case, the survival period from the onset of symptoms has been over 7 years, despite incomplete resection. Based on the 15 published cases, the prognosis is poorer when the tumor is unresected or incompletely resected, but under favorable circumstances, prolonged survival is possible. Pediatr Pulmonol. 2004; 37:368–374. © 2004 Wiely‐Liss, Inc.