Premium
Congenital pulmonary capillary hemangiomatosis: Report of two cases and review of the literature
Author(s) -
Oviedo Angelica,
Abramson Lisa P.,
Worthington Ross,
Dainauskas John R.,
Crawford Susan E.
Publication year - 2003
Publication title -
pediatric pulmonology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.866
H-Index - 106
eISSN - 1099-0496
pISSN - 8755-6863
DOI - 10.1002/ppul.10245
Subject(s) - medicine , neovascularization , pulmonary hypertension , pathology , cardiology , angiogenesis
Pulmonary capillary hemangiomatosis (PCH) is a rare disease characterized by pulmonary hypertension and excessive neovascularization within the pulmonary interstitium, vasculature, and airways. We describe two unusual cases of congenital PCH. Both cases had concurrent anomalies, including renal and urinary bladder agenesis and hypertropic cardiomyopathy. In one case, capillary proliferation caused significant impingement of the proximal bronchial airways. A review of the current literature is described. Pediatr Pulmonol. 2003; 36:253–256. © 2003 Wiley‐Liss, Inc.