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Primary pulmonary lymphangiectasis in a premature infant: Resolution following intensive care
Author(s) -
Scott C.,
Wallis C.,
Dinwiddie R.,
Owens C.,
Coren M.
Publication year - 2003
Publication title -
pediatric pulmonology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.866
H-Index - 106
eISSN - 1099-0496
pISSN - 8755-6863
DOI - 10.1002/ppul.10241
Subject(s) - medicine , intensive care , intensive care medicine , respiratory disease , pediatrics , lung
Primary pulmonary lymphangiectasis is a rare disease, often described as fatal within the neonatal period. We report on an infant who developed severe bilateral chylous pleural effusions with computed tomography (CT) features of pulmonary lymphangiectasis. She recovered spontaneously with supportive treatment only. We discuss aspects of her intensive care which might have contributed to the good outcome, and conclude that modern intensive care may allow spontaneous recovery in conditions described in the literature as having a very poor outcome. Pediatr Pulmonol. 2003; 35:405–406. © 2003 Wiley‐Liss, Inc.