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Recurrent unilateral bacterial pneumonias and interstitial fibrosis associated with pulmonary vein atresia: Successful treatment with endovascular stent implantation
Author(s) -
Sacco O.,
Fregonese B.,
Fregonese L.,
Gambini C.,
Pongiglione G.,
Rossi G.A.
Publication year - 2002
Publication title -
pediatric pulmonology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.866
H-Index - 106
eISSN - 1099-0496
pISSN - 8755-6863
DOI - 10.1002/ppul.10158
Subject(s) - medicine , lung , stent , lung biopsy , pulmonary atresia , cardiac catheterization , cardiology , pulmonary fibrosis , right pulmonary artery , pulmonary angiography , pulmonary artery , radiology , atresia
Abstract A variety of pulmonary vascular disorders, such as hemangiomatosis, telangectasia, and veno‐occlusive disease, may be involved in the pathogenesis of interstitial lung diseases. We describe the case of a girl with recurrent bacterial pneumonia and progressive interstitial fibrosis affecting the right lung. Morphologic evaluation of the lung biopsy showed structural changes of the vessel walls suggesting pulmonary hypertension. The echocardiogram showed the presence of centripetal blood flow in the right pulmonary artery from the periphery of the lung to the heart. A selective right angiography demonstrated the presence of pulmonary venous obstruction at the veno‐atrial junction, successfully treated by endovascular stent implantation during cardiac catheterization. Pediatr Pulmonol. 2002; 34:324–328. © 2002 Wiley‐Liss, Inc.