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Prenatally diagnosed portocaval shunt and postnatal outcome: a case report
Author(s) -
Manning Nicky,
Impey Lawrence,
Lindsell David,
Lakhoo Kokila
Publication year - 2004
Publication title -
prenatal diagnosis
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.956
H-Index - 97
eISSN - 1097-0223
pISSN - 0197-3851
DOI - 10.1002/pd.947
Subject(s) - medicine , ductus venosus , inferior vena cava , porta hepatis , umbilical vein , shunt (medical) , surgery , inferior mesenteric vein , splenic vein , portal venous system , portal venous pressure , portacaval shunt , fetus , cardiology , radiology , pregnancy , portal vein , portal hypertension , cirrhosis , biochemistry , genetics , chemistry , in vitro , biology
Abstract Congenital absence of the portal vein (CAPV) is a rare anomaly in the form of a portocaval shunt, whereby the intestinal and splenic venous drainage bypasses the liver and drains directly into the systemic circulation. We report a case of CAPV diagnosed prenatally after the recognition of a dilated umbilical vein draining directly into a large inferior vena cava (IVC). The IVC then drained into the right atrium of a dilated, hyperdynamic heart. The ductus venosus could not be identified. Repeated postnatal scans showed a gradual disappearance of venous lakes in the region of the porta hepatis and a clear drainage of the splenic vein to the left renal vein and the superior mesenteric vein to the IVC. From birth up to twelve months follow‐up there was no evidence of liver dysfunction, encephalopathy or liver lesions. Copyright © 2004 John Wiley & Sons, Ltd.