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Thymoma and thymic carcinoma in children and adolescents: The EXPeRT/PARTNER diagnostic and therapeutic recommendations
Author(s) -
StachowiczStencel Teresa,
Synakiewicz Anna,
Cornet Marianna,
Ferrari Andrea,
Garassino Marina,
Masip Jordi Remon,
Rod Julien,
Virgone Calogero,
Schneider Dominik T.,
Brecht Ines B.,
BenAmi Tal,
Bien Ewa,
Reguerre Yves,
Godzinski Jan,
Bisogno Gianni,
Orbach Daniel,
Sarnacki Sabine
Publication year - 2021
Publication title -
pediatric blood and cancer
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.116
H-Index - 105
eISSN - 1545-5017
pISSN - 1545-5009
DOI - 10.1002/pbc.29042
Subject(s) - thymic carcinoma , medicine , thymoma , anterior mediastinum , thymus neoplasm , mediastinum , pathology , pediatrics , surgery
Thymic tumors are epithelial tumors arising from the anterior mediastinum and constitute 0.2–1.5% of all adult malignancies but are exceptional in pediatric population. Thymic epithelial tumors (TETs) encompass a variety of histologic subtypes associated with different clinical outcomes. Due to its rarity in children, TETs’ management requires a multidisciplinary approach. However, prognosis remains still poor, especially among patients with thymic carcinoma. This study presents the internationally recognized recommendations for the diagnosis and treatment of thymic tumors in children and adolescents, established by the European Cooperative Study Group for Pediatric Rare Tumors (EXPeRT) group within the EU‐funded project Paediatric Rare Tumours Network ‐ European Registry (PARTNER).