Premium
Histiocytic sarcoma in a child—successful management and long‐term survival with cytoreductive surgery and hyperthermic intraperitoneal chemotherapy
Author(s) -
Sandler Gideon,
Franklin Anna,
HayesJordan Andrea
Publication year - 2018
Publication title -
pediatric blood and cancer
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.116
H-Index - 105
eISSN - 1545-5017
pISSN - 1545-5009
DOI - 10.1002/pbc.27054
Subject(s) - medicine , histiocytic sarcoma , sarcoma , chemotherapy , histiocyte , cytoreductive surgery , hyperthermic intraperitoneal chemotherapy , surgery , blood cancer , presentation (obstetrics) , lymph , disease , pathology , cancer , ovarian cancer
Histiocytic sarcoma is an extremely rare tumor in children. It may occur sporadically or in association with other hematological malignancies. It arises most commonly in the lymph nodes but may occur anywhere in the body and clinical presentation is usually with advanced disease. Following tissue diagnosis and staging, management is with chemotherapy though there are no standard regimes. Surgery has been used successfully for local control. This is the first description of the use of peritonectomy and hyperthermic intraperitoneal chemotherapy to treat histiocytic sarcoma. The 4‐year‐old patient has been disease free for 6 years.