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A single‐center experience with undifferentiated embryonal sarcoma of the liver
Author(s) -
Mathias Melissa D.,
Ambati Srikanth R.,
Chou Alexander J.,
Slotkin Emily K.,
Wexler Leonard H.,
Meyers Paul A.,
Magnan Heather
Publication year - 2016
Publication title -
pediatric blood and cancer
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.116
H-Index - 105
eISSN - 1545-5017
pISSN - 1545-5009
DOI - 10.1002/pbc.26154
Subject(s) - medicine , single center , embryonal rhabdomyosarcoma , center (category theory) , sarcoma , oncology , pathology , rhabdomyosarcoma , chemistry , crystallography
Undifferentiated embryonal sarcoma of the liver (UESL) is a rare aggressive mesenchymal pediatric tumor. Previously, reported outcomes have been very poor. Here, we report a single‐center experience of five patients with UESL treated with upfront gross total resection and adjuvant chemotherapy. We have a median follow‐up of 8 years with a range from 5 to 19 years with 100% event‐free survival.