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Solitary, extracutaneous, skull‐based juvenile xanthogranuloma
Author(s) -
De Paula André Maues,
André Nicolas,
Fernandez Carla,
Coulibaly Bema,
Scavarda Didier,
Lena Gabriel,
Bouvier Corinne
Publication year - 2010
Publication title -
pediatric blood and cancer
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.116
H-Index - 105
eISSN - 1545-5017
pISSN - 1545-5009
DOI - 10.1002/pbc.22534
Subject(s) - juvenile xanthogranuloma , skull , medicine , lesion , radiation therapy , magnetic resonance imaging , posterior fossa , anatomy , pathology , radiology , histiocyte
We report a case of an 18‐month‐old female who presented an occipital bone lesion with progressive growth. Imaging studies showed a left extradural, skull‐based tumor partially occupying the posterior fossa. Histopathological and immunohistochemical studies confirmed a juvenile xanthogranuloma (JXG). Partial surgical resection, chemotherapy, and conformational radiotherapy were used. Exclusive extracutaneous JXG with an intracranial, vertebral, or skull‐based localization is extremely rare. Pediatr Blood Cancer. 2010;55:380–382. © 2010 Wiley–Liss, Inc.