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A composite pheochromocytoma/ganglioneuroblastoma of the adrenal gland
Author(s) -
Thiel Elizabeth Lee,
Trost Beth A.,
Tower Richard L.
Publication year - 2010
Publication title -
pediatric blood and cancer
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.116
H-Index - 105
eISSN - 1545-5017
pISSN - 1545-5009
DOI - 10.1002/pbc.22436
Subject(s) - ganglioneuroblastoma , medicine , pheochromocytoma , adrenal gland , abdominal mass , population , neuroblastoma , pathology , ganglioneuroma , genetics , environmental health , biology , cell culture
Abstract A 9‐year‐old female presented with a large abdominal mass. At surgery, the mass was noted to arise from the right adrenal gland. As the mass was manipulated, the patient developed severe hypertension. The final diagnosis was a cystic composite‐pheochromocytoma/ganglioneuroblastoma. This compound adrenal tumor is only the fourth case reported in a child. Because composite pheochromocytomas are rare in the pediatric population, the management, optimal surveillance schedule and outcomes have not been characterized. Pediatr Blood Cancer 2010;54:1032–1034 © 2010 Wiley‐Liss, Inc.