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Sister Mary Joseph's nodule as presenting sign of a desmoplastic small round cell tumor
Author(s) -
Doros Leslie,
Kaste Sue C.,
RodriguezGalindo Carlos
Publication year - 2008
Publication title -
pediatric blood and cancer
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.116
H-Index - 105
eISSN - 1545-5017
pISSN - 1545-5009
DOI - 10.1002/pbc.20915
Subject(s) - desmoplastic small round cell tumor , medicine , malignancy , nodule (geology) , abdominal mass , lesion , abdomen , population , sister , pathology , disease , radiology , sarcoma , biology , paleontology , environmental health , sociology , anthropology
Umbilical metastases, also named Sister Mary Joseph's nodules, are well documented in the adult population and most often represent an underlying intra‐abdominal malignancy, usually a carcinoma of gastrointestinal or gynecologic origin. They are indicative of widespread abdominal disease and are associated with a poor prognosis. An extensive review of the literature reveals only two such presentations in the pediatric population. A 14‐year‐old male presented with an umbilical mass, which was found to be a metastatic lesion of a desmoplastic small round cell tumor (DSRCT) of the abdomen. The diagnosis of an intra‐abdominal malignancy, most commonly a DSRCT, should be considered in the presence of an umbilical mass in a child. Pediatr Blood Cancer 2008;50:388–390. © 2006 Wiley‐Liss, Inc.