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Primary malignant peripheral nerve sheath tumor of the lung in a young child without neurofibromatosis type 1
Author(s) -
Muwakkit Samar A.,
RodriguezGalindo Carlos,
EL Samra Ahmad I.,
Khoury Ruby,
Akel Samir R.,
Mroueh Salman,
Razzouk Bassem,
Abboud Miguel R.
Publication year - 2006
Publication title -
pediatric blood and cancer
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.116
H-Index - 105
eISSN - 1545-5017
pISSN - 1545-5009
DOI - 10.1002/pbc.20787
Subject(s) - medicine , neurofibromatosis , malignant peripheral nerve sheath tumor , differential diagnosis , lung , pathology , peripheral , lung cancer , radiology
Malignant peripheral nerve sheath tumors (MPNST) are uncommon in children and almost half of the cases occur in patients with neurofibromatosis 1 (NF1). We report a child with a primary MPNST of the lung without NF1. MPNST of the lung has similar clinical and radiologic characteristics as pleuropulmonary blastoma. We suggest to include MPNST of the lung in the differential diagnosis of intrapulmonary masses in children. Pediatr Blood Cancer 2006; 47:636–638. © 2006 Wiley‐Liss, Inc.