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Rhabdomyosarcoma arising within congenital cystic adenomatoid malformation
Author(s) -
Pai Shyun,
Eng HockLiew,
Lee ShinYi,
Hsiao ChihCheng,
Huang WanTing,
Huang ShunChen
Publication year - 2005
Publication title -
pediatric blood and cancer
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.116
H-Index - 105
eISSN - 1545-5017
pISSN - 1545-5009
DOI - 10.1002/pbc.20481
Subject(s) - medicine , rhabdomyosarcoma , embryonal rhabdomyosarcoma , congenital cystic adenomatoid malformation , chemotherapy , surgical resection , rare disease , surgery , radiology , sarcoma , disease , pathology , pregnancy , fetus , biology , genetics
Rhabdomyosarcoma arising within a congenital cystic adenomatoid malformation (CCAM) is an unusual entity. The patient underwent a lobectomy of his right lower lobe of lung due to a CCAM at the age of two. One year later, he developed a solid embryonal rhabdomyosarcoma at the same location. He received 1‐year period chemotherapy and when the tumor reduced to a resectable size, surgical excision was done. The tumor cells appeared more differentiated after chemotherapy. The patient remains disease free to date, 16 months after surgery. © 2005 Wiley‐Liss, Inc.
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