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Transient paresis in myotonic syndromes: A simplified electrophysiologic approach
Author(s) -
Streib Erich W.,
Sun Sallie F.,
Yarkowsky Tony
Publication year - 1982
Publication title -
muscle and nerve
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.025
H-Index - 145
eISSN - 1097-4598
pISSN - 0148-639X
DOI - 10.1002/mus.880050909
Subject(s) - myotonia , compound muscle action potential , isometric exercise , paresis , medicine , ulnar nerve , wrist , electromyography , myotonia congenita , physical medicine and rehabilitation , anesthesia , myotonic dystrophy , cardiology , anatomy , electrophysiology , surgery , elbow
Patients with different myotonic syndromes were evaluated for the presence of transient decrease of muscle fiber excitability. The evoked compound muscle action potential (CMAP) was recorded from the hypothenar eminence; single, supramaximal stimuli were applied to the ulnar nerve at the wrist before and after various periods of voluntary, isometric exercise of the hand muscles. A variable decline of the CMAP after exercise was present in all subjects with myotonia. The results were similar to those obtained with rapid repetitive nerve stimulation.