Premium
Acute motor axonal neuropathy in association with Sjögren syndrome
Author(s) -
Awad Amer,
Mathew Sani,
Katirji Bashar
Publication year - 2010
Publication title -
muscle and nerve
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.025
H-Index - 145
eISSN - 1097-4598
pISSN - 0148-639X
DOI - 10.1002/mus.21830
Subject(s) - medicine , xerophthalmia , fulminant , acute motor axonal neuropathy , pathological , peripheral neuropathy , peripheral nervous system , guillain barre syndrome , axonal degeneration , neurology , pathology , pediatrics , central nervous system , endocrinology , diabetes mellitus , vitamin a deficiency , retinol , psychiatry , vitamin
Sjögren syndrome (SS) has been known to manifest with neurological complications, most frequently of the peripheral nervous system, and often in advance of xerostomia and xerophthalmia. There has been one case report of a patient with SS presenting with acute motor neuropathy similar to Guillain–Barré syndrome (GBS). We report the case of a patient who developed rapidly fulminant acute motor axonal neuropathy (AMAN) with positive anti‐GM1 antibody at high titers in association with serological and pathological evidence of SS without xerostomia or xerophthalmia. Muscle Nerve 42: 828–832, 2010