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Adductor laryngeal breathing dystonia in a patient with lubag (X‐linked dystonia‐parkinsonism syndrome)
Author(s) -
Lew M. F.,
Shindo M.,
Moskowitz C. B.,
Wilhelmsen K. C.,
Fahn S.,
Waters C. H.
Publication year - 1994
Publication title -
movement disorders
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 3.352
H-Index - 198
eISSN - 1531-8257
pISSN - 0885-3185
DOI - 10.1002/mds.870090307
Subject(s) - dystonia , botulinum toxin , medicine , stridor , parkinsonism , anesthesia , neurological disorder , breathing , larynx , surgery , central nervous system disease , airway , disease , psychiatry
We report a patient with Lubag (X‐linked dystonia‐parkinsonism) who presented with severe respiratory stridor form adductor laryngeal breathing dystonia. Emergency tracheostomy was necessary, and subsequent laryngeal injection with botulinum toxin led to worsening aspiration. Botulinum toxin injection for severe lingual dystonia was successful.