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Creutzfeldt‐Jakob's disease presenting with ataxia and a movement disorder
Author(s) -
Sethi Kapil D.,
Hess David C.
Publication year - 1991
Publication title -
movement disorders
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 3.352
H-Index - 198
eISSN - 1531-8257
pISSN - 0885-3185
DOI - 10.1002/mds.870060212
Subject(s) - dystonia , ataxia , movement disorders , dementia , differential diagnosis , autopsy , disease , medicine , myoclonus , creutzfeldt jakob syndrome , degenerative disease , neurological disorder , pediatrics , central nervous system disease , pathology , psychiatry , surgery , prion protein
We describe a 62‐year‐old patient who presented with ataxia and dystonia with mild dementia and was shown at autopsy to have Creutzfeldt‐Jakob's disease. Movement disorders may be the presenting feature of Creutzfeldt‐Jakob's disease, and this entity should be considered in the differential diagnosis of an otherwise obscure movement disorder even when the typical electroencephalographic pattern is absent.