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Limb amputations in fixed dystonia: A form of body integrity identity disorder?
Author(s) -
Edwards Mark J.,
AlonsoCanovas Araceli,
Schrag Arnette,
Bloem Bastiaan R.,
Thompson Philip D.,
Bhatia Kailash
Publication year - 2011
Publication title -
movement disorders
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 3.352
H-Index - 198
eISSN - 1531-8257
pISSN - 0885-3185
DOI - 10.1002/mds.23671
Subject(s) - dystonia , amputation , medicine , context (archaeology) , physical medicine and rehabilitation , psychology , physical therapy , surgery , psychiatry , paleontology , biology
Abstract Fixed dystonia is a disabling disorder mainly affecting young women who develop fixed abnormal limb postures and pain after apparently minor peripheral injury. There is continued debate regarding its pathophysiology and management. We report 5 cases of fixed dystonia in patients who sought amputation of the affected limb. We place these cases in the context of previous reports of patients with healthy limbs and patients with chronic regional pain syndrome who have sought amputation. Our cases, combined with recent data regarding disorders of mental rotation in patients with fixed dystonia, as well as previous data regarding body integrity identity disorder and amputations sought by patients with chronic regional pain syndrome, raise the possibility that patients with fixed dystonia might have a deficit in body schema that predisposes them to developing fixed dystonia and drives some to seek amputation. The outcome of amputation in fixed dystonia is invariably unfavorable. © 2011 Movement Disorder Society