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Extraocular muscle dystonia due to acquired (non‐Wilsonian) hepatocerebral degeneration
Author(s) -
Ferrara Joseph,
Gupta Deepak,
Foster Emily,
Garman Katherine,
Stacy Mark
Publication year - 2008
Publication title -
movement disorders
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 3.352
H-Index - 198
eISSN - 1531-8257
pISSN - 0885-3185
DOI - 10.1002/mds.21841
Subject(s) - dystonia , extraocular muscles , neurological disorder , medicine , focal dystonia , movement disorders , differential diagnosis , dyskinesia , central nervous system disease , physical medicine and rehabilitation , surgery , pathology , disease , parkinson's disease , psychiatry
We present a video report of a patient with advanced non‐Wilsonian cirrhotic liver disease who developed extraocular muscle dystonia (oculogyric crisis) and severe orofaciolingual dyskinesias. Acquired hepatocerebral degeneration causes choreic movements, especially of cranial muscles, but dystonic ocular spasm is an infrequent manifestation of this disorder. This case illustrates that AHD should be considered in the differential diagnosis of extraocular muscle dystonia. © 2008 Movement Disorder Society