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Cruveilhier‐Baumgarten disease in a patient with turner syndrome: Case report of a rare indication for liver transplantation
Author(s) -
Aucejo Federico,
Ibrahim Zuhaib,
Hashimoto Koji,
Quintini Cristiano,
Kelly Dympna,
Vogt David,
Eghtesad Bijan,
Fung John,
Miller Charles,
Tuthill Ralph
Publication year - 2008
Publication title -
liver transplantation
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.814
H-Index - 150
eISSN - 1527-6473
pISSN - 1527-6465
DOI - 10.1002/lt.21374
Subject(s) - medicine , liver transplantation , portal hypertension , hypoplasia , liver disease , agenesis , liver function , transplantation , portal venous pressure , disease , cardiology , gastroenterology , surgery , cirrhosis
Some chromosomal alterations can be associated with vascular abnormalities. For instance, Turner syndrome can be complicated by agenesis or hypoplasia of the portal venous system causing presinusoidal portal hypertension. Liver transplantation to treat this condition overcomes portal hypertension and reconstitutes the diminished hepatic function due to severe atrophy of the portal venous inflow. Liver Transpl 14:299–302, 2008. © 2008 AASLD.