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Eosinophilic Granulomatosis With Polyangiitis: An Unusual Case of Pediatric Subglottic Stenosis
Author(s) -
Mokhtari Tara E.,
Miller Lauren E.,
Jayawardena Asitha D. L.,
Sadow Peter M.,
Hardy Stephen C.,
Rothman Deborah,
Hartnick Christopher J.
Publication year - 2021
Publication title -
the laryngoscope
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.181
H-Index - 148
eISSN - 1531-4995
pISSN - 0023-852X
DOI - 10.1002/lary.28848
Subject(s) - granulomatosis with polyangiitis , medicine , subglottic stenosis , eosinophilic , stridor , context (archaeology) , systemic vasculitis , dermatology , systemic disease , stenosis , vasculitis , disease , pathology , airway , surgery , paleontology , biology
Systemic disease is an uncommon cause of subglottic stenosis (SGS). We report a case of severe SGS due to underlying eosinophilic granulomatosis with polyangiitis (EGPA) in a child presenting with isolated stridor. EGPA is a rare systemic vasculitis with very limited cases reported in the pediatric population. While surgical intervention was required given the degree of stenosis in this case, medical management of the underlying systemic disease process is critical when there is clinical suspicion of SGS in the context of systemic vasculitis. Laryngoscope , 131:656–659, 2021