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Simulation‐Guided Tracheotomy in a Patient With Fibrodysplasia Ossificans Progressiva
Author(s) -
Padia Reema,
Miller Craig,
Patak Lance,
Friedman Seth D.,
Stone Kimberly,
Otjen Jeffrey,
Johnson Kaalan
Publication year - 2019
Publication title -
the laryngoscope
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.181
H-Index - 148
eISSN - 1531-4995
pISSN - 0023-852X
DOI - 10.1002/lary.27520
Subject(s) - medicine , fibrodysplasia ossificans progressiva , tracheotomy , trismus , heterotopic bone , surgery , myositis ossificans , airway , computed tomography , radiology , heterotopic ossification
Fibrodysplasia ossificans progressiva (FOP) is a rare disorder that causes heterotopic bone formation leading to chest wall and spinal deformities. This case describes an 11‐year‐old female with FOP who presented in respiratory failure necessitating two emergent fiberoptic nasotracheal intubations. The patient had severe trismus, rotary flexion of the neck, and distortion of the airway. A three‐dimensional printed model based off of a computed tomography reconstruction was created for an in situ simulation before the true procedure. The surgery and trach change were both uneventful. We propose that with careful preoperative planning, tracheotomy can be an appropriate option for FOP patients. Laryngoscope , 129:812–817, 2019