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A newborn with three cochlear turns: Case report and literature review
Author(s) -
Hildrew Douglas M.,
Ananth Ashwin,
Rodriguez Kimsey H.
Publication year - 2016
Publication title -
the laryngoscope
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.181
H-Index - 148
eISSN - 1531-4995
pISSN - 0023-852X
DOI - 10.1002/lary.25560
Subject(s) - cochlea , cochlear implantation , hypoplasia , medicine , audiology , hearing loss , anatomy
Objectives/Hypothesis The human cochlea is most commonly considered to have two and a half turns. Although the causes of cochlear hypoplasia are well described, cochlear hyperplasia is a rarer entity that is poorly understood. We describe rare anatomic cochlear malformations identified in a 4‐month‐old male originally referred for evaluation after a failed newborn hearing screening. The full diagnostic evaluation, imaging findings, treatment, and follow‐up are described in detail. Cochleae with three turns are an uncommon malformation that is not included in current classifications schemes and may represent a distinct type of anomaly not caused by developmental arrest. Laryngoscope , 126:469–471, 2016