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Hemangiopericytoma of the uterus: Report of a case with a comprehensive review of the literature
Author(s) -
Sooriyaarachchi Gamini S.,
Ramirez Guillermo,
Roley Everett L.
Publication year - 1978
Publication title -
journal of surgical oncology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.201
H-Index - 111
eISSN - 1096-9098
pISSN - 0022-4790
DOI - 10.1002/jso.2930100504
Subject(s) - medicine , hemangiopericytoma , radiation therapy , uterus , hysterectomy , chemotherapy , radical surgery , surgery , radiology , cancer
A case of locally recurrent and metastatic uterine hemangiopericytoma successfully treated with surgery, radiotherapy and chemotherapy is presented. The patient is alive without evidence of detectable tumor, 13 years after the initial diagnosis. Review of the literature revealed 64 reported cases of uterine hemangiopericytoma. The clinical features are not sufficiently characteristic to enable the diagnosis to be made preoperatively. However, with the help of histological and ultrastructural studies a definite diagnosis of hemangiopericy toma can be made. The primary treatment is radical surgery which usually involves total hysterectomy and bilateral salpingo‐oophorectomy. The prognosis of uterine hemangiopericy toma is better than that of other sites. However, long follow‐up of these patients is necessary because of the tendency to local and distant recurrence many years after the initial treatment. The recurrent tumor should be treated aggressively with surgery, radiotherapy, and chemotherapy as long‐term survival is not unusual.