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Malignant tumors of blood vessels: Angiosarcomas, hemangioendotheliomas, and hemangioperictyomas
Author(s) -
Koch Moritz,
Nielsen G. Petur,
Yoon Sam S.
Publication year - 2008
Publication title -
journal of surgical oncology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.201
H-Index - 111
eISSN - 1096-9098
pISSN - 0022-4790
DOI - 10.1002/jso.20973
Subject(s) - medicine , hemangiopericytoma , radiation therapy , chemotherapy , sarcoma , angiosarcoma , hemangiosarcoma , radiology , surgery , pathology
Abstract Sarcomas that arise from or resemble the components of blood vessels are uncommon and include angiosarcomas, hemangioendotheliomas, and hemangiopericytomas. This article reviews the management of these three types of sarcomas. Diagnosis can sometimes be difficult, with the diagnosis of hemangiopericytoma versus solitary fibrous tumor currently in debate. Each of these sarcomas subtypes has certain unique clinical traits. The mainstay of treatment is surgical resection, sometimes combined with radiation therapy. Adjuvant chemotherapy is unproven but can be considered. For patients with advanced disease, various chemotherapeutic regimens may result in meaningful responses in a minority of patients. J. Surg. Oncol. 2008;97:321–329. © 2008 Wiley‐Liss, Inc.