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Clear cell sarcoma of soft tissues
Author(s) -
Malchau Sara Sofia,
Hayden James,
Hornicek Francis,
Mankin Henry J.
Publication year - 2006
Publication title -
journal of surgical oncology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.201
H-Index - 111
eISSN - 1096-9098
pISSN - 0022-4790
DOI - 10.1002/jso.20730
Subject(s) - medicine , sarcoma , adjuvant therapy , soft tissue , lesion , metastasis , soft tissue sarcoma , incidence (geometry) , surgery , clear cell sarcoma , distant metastasis , pathology , chemotherapy , cancer , physics , optics
Clear cell sarcoma (CCS) is a rare but highly malignant tumor of soft tissues often appearing as a small tender mass in the deep tissues of the distal extremities. We have studied 17 patients with such lesions treated since 1986 and have a high incidence of local recurrence and metastasis with a survival rate of only 47% despite surgery and for many of the patients, adjuvant therapy. The purpose of this article is to warn the readers of the dangers related to treating this seemingly benign lesion and urge them to perform wide surgery and utilize adjuvant therapy. J. Surg. Oncol. 2007; 95: 519–522. © 2006 Wiley‐Liss, Inc.