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Cystic lymphangiomatosis with severe intra‐abdominal bleeding in a newborn: Case report
Author(s) -
Baskın Didem,
Narcı Adnan,
Okur Nazan,
Uğraş Meltem,
Nadirgil Köken Gülengül,
Ali Tuncer Ahmet,
Tokyol Çiğdem,
Çetinkurşun Salih
Publication year - 2013
Publication title -
journal of clinical ultrasound
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.272
H-Index - 61
eISSN - 1097-0096
pISSN - 0091-2751
DOI - 10.1002/jcu.21956
Subject(s) - lymphangiomatosis , medicine , meconium , meconium peritonitis , abdominal distension , abdominal ultrasound , meconium ileus , perforation , prenatal diagnosis , abdominal ultrasonography , pregnancy , abdominal pain , neonatology , surgery , fetus , ultrasonography , pathology , lymphatic system , biology , metallurgy , punching , genetics , materials science
We report the case of a newborn girl with intestinal cystic lymphangiomatosis who presented with abdominal distension and intra‐abdominal bleeding following a prenatal ultrasound diagnosis of intestinal anomaly. Postnatal abdominal ultrasound revealed disseminated submucosal and intramural cystic dilatations of various sizes in the bowel and intestinal lymphangiomatosis was diagnosed. The presence of severe bleeding diathesis and widespread disease led to conservative treatment. The patient died on postnatal day 7 and postmortem examination confirmed cystic lymphangiomatosis. Detection of intestinal hyperechogenicity and/or dilatation in prenatal ultrasonography and the persistence of these findings during pregnancy are suggestive for pathologies such as meconium ileus, meconium peritonitis, and intestinal atresia. Although rare, intestinal lymphangiomatosis should be kept in mind in patients whose prenatal sonographic findings persist until birth. © 2012 Wiley Periodicals, Inc. J Clin Ultrasound, 2013