Uterus didelphys with blind hemivagina and ipsilateral renal agenesis (Herlyn‐Werner‐Wunderlich syndrome) suspected on the presence of hydrocolpos on prenatal sonography

We report the case of a female neonate with ipsilateral renal agenesis and uterus didelphys with blind hemivagina, also known as Herlyn‐Werner‐Wunderlich (HWW) syndrome. Prenatal sonography revealed the absence of the left kidney and a retrovesical cystic lesion suspected as hydrometrocolpos. Postnatal evaluation confirmed that the cystic lesion was a hydrocolpos associated with double uterus and blind hemivagina (HWW syndrome). HWW syndrome can be suspected prenatally if a retrovesical cystic lesion is detected in a female fetus with unilateral absence of kidney. © 2012 Wiley Periodicals, Inc. J Clin Ultrasound 41 :380–382, 2013