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Biliary dilatation secondary to lithiasis in a child affected by Langerhans' cell histiocytosis
Author(s) -
Caruso Settimo,
Miraglia Roberto,
Spada Marco,
Luca Angelo,
Gridelli Bruno
Publication year - 2009
Publication title -
journal of clinical ultrasound
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.272
H-Index - 61
eISSN - 1097-0096
pISSN - 0091-2751
DOI - 10.1002/jcu.20574
Subject(s) - medicine , langerhans cell histiocytosis , liver transplantation , jaundice , histiocytosis , common bile duct , anastomosis , obstructive jaundice , bile duct , radiology , gastroenterology , surgery , transplantation , disease
Langerhans' cell histiocytosis (LCH) is a disease of unknown pathogenesis, caused by clonal proliferation of Langerhans' cells. Liver involvement results in a cholangiopathy, which has the radiologic appearance of sclerosing cholangitis. Only 1 case of obstructive jaundice due to common bile duct stone in a patient with LCH has been described. We present a case of a 31‐month‐old child with LCH and liver involvement on the waiting list for liver transplantation. During the follow‐up, there was a rapid onset of jaundice due to sludge and lithiasis. The patient was treated first with an endoscopic biliary plastic stent and then with percutaneous biliary drainage and bilioenteric anastomosis. © 2009 Wiley Periodicals, Inc. J Clin Ultrasound 2009