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Two dimensional echocardiographic similarity of Fabry's disease to cardiac amyloidosis: A function of ultrastructural analogy?
Author(s) -
Cohen Ira S.,
FluriLundeen Joan,
Wharton Thomas P.
Publication year - 1983
Publication title -
journal of clinical ultrasound
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.272
H-Index - 61
eISSN - 1097-0096
pISSN - 0091-2751
DOI - 10.1002/jcu.1870110806
Subject(s) - medicine , medical school , section (typography) , cardiology , library science , gerontology , medical education , computer science , operating system
A 53-year-old man with Fabry's disease was studied by echocardiography. Both M-mode and two dimensional echocardiographic examinations produced findings indistinguishable from those previously described as virtually diagnostic of cardiac amyloidosis. Possible causes for the "granular sparkling" appearance and clinical implications of the similarities were discussed.

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