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Congenital middle ear encephalocele initially seen with facial paresis
Author(s) -
Uri Nechama,
Shupak Avi,
Greenberg Elhanan,
Kelner Judith
Publication year - 1991
Publication title -
head and neck
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.012
H-Index - 127
eISSN - 1097-0347
pISSN - 1043-3074
DOI - 10.1002/hed.2880130110
Subject(s) - medicine , encephalocele , paresis , dehiscence , middle ear , conductive hearing loss , serous fluid , anatomy , meningitis , facial nerve , surgery , pathology
Abstract Congenital middle ear encephalocele (CMEE) is a rare entity, previously reported in only 29 patients. It might originate from dehiscence of the tegmen tympani or antri or the bony plate of the posterior fossa. The common presenting symptoms are spontaneous cerebrospinal fluid (CSF) otorrhea and/or rhinor‐rhea, persistent “serous otitis media,” conductive hearing loss, and, occasionally, recurrent meningitis. We report a case of CMEE initially seen with progressive facial paresis, review the previously reported cases of CMEE, and discuss the pathogenesis and surgical management.