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Enchondroma of the nasal septum due to Ollier disease: A case report and review of the literature
Author(s) -
Jacobi Christian M. C.,
Hiranya Egodage Samitha,
Gay Annietta,
Holzmann David,
Kollias Spyridon,
Soyka Michael B.
Publication year - 2015
Publication title -
head and neck
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.012
H-Index - 127
eISSN - 1097-0347
pISSN - 1043-3074
DOI - 10.1002/hed.23783
Subject(s) - enchondroma , medicine , malignancy , malignant transformation , chondrosarcoma , nose , nasal septum , chondroma , skull , radiology , surgery , pathology
Background Morbus Ollier is characterized by the presence of multiple enchondromas (ie, benign intraosseous cartilaginous lesions). Although their manifestation in the limb bones is well described, only a few cases with ear, nose, and throat (ENT) involvement, primarily arising from the skull, have been reported. The malignant transformation toward slowly growing low‐grade chondrosarcomas is the most severe form of progression. Methods We report a unique case of a 54‐year‐old patient with Ollier disease with an extensive nasal enchondroma apparently eroding the middle nasal concha and expanding to the lateral nasal wall that raised suspicion of malignant transformation. Results Radiological and histological features of enchondromas can be controversial and seem to have limited sensitivity to exclude low‐grade malignancy. The clinical symptoms play a decisive role in differentiation between enchondromas and low‐grade chondrosarcomas. Conclusion Surgery remains the only effective solution in removing an enchondroma and preventing the tendency toward malignant transformation. © 2014 Wiley Periodicals, Inc. Head Neck 37: E30–E33, 2015