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Sporadic endolymphatic sac tumor: Its clinical, radiological, and histological features, management, and follow‐up
Author(s) -
Poletti Arturo M.,
Dubey Siba P.,
Barbò Regina,
Pericotti Sergio,
Fiamengo Barbara,
Colombo Giovanni,
Scorsetti Marta,
Lorusso Rosaria,
Mazzoni Antonio
Publication year - 2013
Publication title -
head and neck
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.012
H-Index - 127
eISSN - 1097-0347
pISSN - 1043-3074
DOI - 10.1002/hed.22962
Subject(s) - medicine , tinnitus , radiological weapon , endolymphatic sac , temporal bone , vertigo , surgery , sensorineural hearing loss , radiation therapy , cerebellopontine angle , hearing loss , skull , posterior cranial fossa , radiology , magnetic resonance imaging , audiology , inner ear
Background Sporadic endolymphatic sac tumor (ELST) is rare. We described the clinical, radiological, and histological features, treatment, and follow‐up of ELST. Method This was a retrospective analysis of 7 cases of sporadic ELST that were managed between 1993 and 2010. Results Twenty‐five to 75 years was the age range of the patients. Subjective hearing loss and tinnitus were the most common presenting features. Five patients had total deafness and 2 had severe sensorineural hearing loss. The most common radiological feature was temporal bone destruction with tumor extension to cerebellopontine angle and posterior cranial fossa. Cholesterol or hemosiderin cysts around the tumor could be a characteristic feature. Major skull base procedures were performed in all 7 cases, and complete tumor excision was achieved in 6 of them. One patient needed a second surgery after she was referred to us after an incomplete first surgery. Recurrences were detected in 2 patients during follow‐up; 1 of them received irradiation without minimal change to the tumor size and the second refused any treatment for the recurrence. Both of them are alive with disease. Conclusion Early detection and radical surgical excision at first attempt give best results. Radiotherapy could be considered only in unresectable recurrences. © 2012 Wiley Periodicals, Inc. Head Neck, 2013