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Definition and treatment of arrhythmogenic cardiomyopathy: an updated expert panel report
Author(s) -
Elliott Perry M.,
Anastasakis Aris,
Asimaki Angeliki,
Basso Cristina,
Bauce Barbara,
Brooke Matthew A.,
Calkins Hugh,
Corrado Domenico,
Duru Firat,
Green Kathleen J.,
Judge Daniel P.,
Kelsell David,
Lambiase Pier D.,
McKenna William J.,
Pilichou Kalliopi,
Protonotarios Alexandros,
Saffitz Jeffrey E.,
Syrris Petros,
Tandri Hari,
Te Riele Anneline,
Thiene Gaetano,
Tsatsopoulou Adalena,
van Tintelen J. Peter
Publication year - 2019
Publication title -
european journal of heart failure
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 5.149
H-Index - 133
eISSN - 1879-0844
pISSN - 1388-9842
DOI - 10.1002/ejhf.1534
Subject(s) - medicine , terminology , disease , cardiomyopathy , intensive care medicine , heart failure , cardiology , philosophy , linguistics
It is 35 years since the first description of arrhythmogenic right ventricular cardiomyopathy (ARVC) and more than 20 years since the first reports establishing desmosomal gene mutations as a major cause of the disease. Early advances in the understanding of the clinical, pathological and genetic architecture of ARVC resulted in consensus diagnostic criteria, which proved to be sensitive but not entirely specific for the disease. In more recent years, clinical and genetic data from families and the recognition of a much broader spectrum of structural disorders affecting both ventricles and associated with a propensity to ventricular arrhythmia have raised many questions about pathogenesis, disease terminology and clinical management. In this paper, we present the conclusions of an expert round table that aimed to summarise the current state of the art in arrhythmogenic cardiomyopathies and to define future research priorities.