Open AccessAnomalous origin of the right coronary artery from the main pulmonary artery: Diagnosis and management
Author(s) -
Hekmat Vahid,
Rao Sudha M.,
Chhabra Manoj,
Chiavarelli Mario,
Anderson John E.,
Nudel Dov B.
Publication year - 1998
Publication title -
clinical cardiology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.263
H-Index - 72
eISSN - 1932-8737
pISSN - 0160-9289
DOI - 10.1002/clc.4960211016
Subject(s) - medicine , asymptomatic , pulmonary artery , cardiology , artery , heart failure , right coronary artery , left coronary artery , right pulmonary artery , right heart failure , coronary angiography , myocardial infarction
Anomalous origin of the right coronary artery (ARCA) from the main pulmonary artery (MPA) is a rare congenital anomaly, with only 18 reported cases in the pediatric age group. More than half of these had associated cardiac anomalies that masked the presence of ARCA. Conversely, in many patients with ARCA as an isolated anomaly, the diagnosis has been missed during lifetime. The only patient with an isolated ARCA who was diagnosed in infancy presented with congestive heart failure. Asymptomatic infants with ARCA from the MPA have not been previously reported. Three additional cases, two infants and a child with ARCA from the MPA, are reported in this paper. The diagnostic dilemmas and the prognosis are discussed and management is recommended.