Open AccessArrhythmogenic right ventricular dysplasia presenting with ventricular tachycardia in a father and son
Author(s) -
BLundqvist C.,
Eneström S.,
Edvardsson N.,
Olsson S. B.
Publication year - 1987
Publication title -
clinical cardiology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.263
H-Index - 72
eISSN - 1932-8737
pISSN - 0160-9289
DOI - 10.1002/clc.4960100415
Subject(s) - medicine , arrhythmogenic right ventricular dysplasia , cardiology , ventricular tachycardia , ventricular function , left bundle branch block , right bundle branch block , tachycardia , fractional shortening , sustained ventricular tachycardia , dysplasia , electrocardiography , cardiac function curve , heart failure , cardiomyopathy
A father and his son presented with ventricular tachycardia of left bundle‐branch block configuration, two years apart. The patients had no clinical signs of right or left ventricular dysfunction. The diagnosis of arrhythmogenic right ventricular dysplasia was based on right ventricular angiographic and radionuclide findings. Microscopic sections obtained at surgery for the ventricular tachycardia in the father revealed abnormal infiltration of fat and focal fibrosis in the right ventricular myocardium, confirming the diagnosis. The importance of thorough evaluation of right and left ventricular function and structure in patients with ventricular tachycardia of right ventricular origin is emphasized. Currently available diagnostic techniques and management are presented.