
An unusual case of Dyke–Davidoff–Masson syndrome revealed by status epilepticus in a Malian patient
Author(s) -
Djimdé Samba O.,
Yalcouyé Abdoulaye,
Koïta Abdou,
Samir Hassana,
Kebkiba Pofinet,
Gueli Chrystelle Awovi,
Maïga Alassane B.,
Sissoko Adama S.,
Landouré Guida
Publication year - 2022
Publication title -
clinical case reports
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.21
H-Index - 9
ISSN - 2050-0904
DOI - 10.1002/ccr3.6428
Subject(s) - status epilepticus , medicine , hemiparesis , facial symmetry , epilepsy , skull , pediatrics , atrophy , surgery , pathology , psychiatry , lesion
The Duke–Davidoff–Masson syndrome (DDMS) is a rare neurological condition with unknown prevalence, globally. To date, <100 cases have been reported worldwide. We report the case of an 18‐year‐old patient admitted for status epilepticus seizure, and who presented a right hemiparesis, body asymmetry, joints ankylosis, and mental retardation. Brain CT‐scan revealed left hemisphere atrophy, skull bone thickening, and hyperpneumatization of the frontal sinuses; all consistent with DDMS. Seizures improved remarkably on Levetiracetam and Valproate. This is the first report of an unusual DDMS in Mali, and the diagnosis delay highlights the challenges for the management of these diseases in resource‐limited settings.