Open AccessErdheim‐Chester disease with long‐standing diabetes insipidus and generalized edema
Author(s) -
Naji Faezeh Sadat,
Hajmiri Minoo Sadat,
Mazari Zahra,
Salahshour Faeze,
Soleimani Vahid,
Nakhjavani Manouchehr,
Hemmatabadi Mahboobeh
Publication year - 2021
Publication title -
clinical case reports
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.21
H-Index - 9
ISSN - 2050-0904
DOI - 10.1002/ccr3.4898
Subject(s) - medicine , diabetes insipidus , erdheim–chester disease , histiocytosis , diabetes mellitus , disease , weakness , surgery , pediatrics , dermatology , pathology , endocrinology
Erdheim‐Chester disease (ECD) is a rare non‐Langerhans histiocytosis. ECD is detected more frequently due to increased awareness of healthcare providers and improved diagnostic tools. This report describes a 51‐year‐old woman with a history of weakness, bone pain, xanthelasma palpebrarum, and diabetes insipidus. ECD is a multisystemic condition with a poor prognosis. This disease should be considered in patients with diabetes insipidus, bone pain, and multiorgan involvements.