
Granulomatosis with polyangiitis (Wegener’s) complicated by splenic rupture and severe acute respiratory distress syndrome: A case report
Author(s) -
Ahmad Yannis,
Morawietz Gabrielle,
Ksouri Hatem,
Schefold Joerg C.,
Zuercher Patrick
Publication year - 2021
Publication title -
clinical case reports
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.21
H-Index - 9
ISSN - 2050-0904
DOI - 10.1002/ccr3.4369
Subject(s) - medicine , granulomatosis with polyangiitis , microscopic polyangiitis , respiratory distress , acute respiratory distress , radiological weapon , disease , dermatology , intensive care medicine , radiology , pathology , vasculitis , lung
Even in the absence of disease‐specific radiological signs of granulomatosis with polyangiitis (GPA), severe intrapulmonary GPA may be present. Rapidly establishing the diagnosis with a confirmatory biopsy is key to initiate lifesaving therapy.