Open AccessSystemic sclerosis with renal crisis and pericardial effusion
Author(s) -
Prudhvi Kalyan,
Jonnadula Jayasree,
Kutti Sridharan Gurusaravanan,
Dominguez Mary
Publication year - 2020
Publication title -
clinical case reports
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.21
H-Index - 9
ISSN - 2050-0904
DOI - 10.1002/ccr3.3467
Subject(s) - medicine , pericardial effusion , pericardiocentesis , cardiac tamponade , scleroderma (fungus) , thrombotic microangiopathy , tamponade , dialysis , pericarditis , pericardial window , cardiology , pathology , disease , inoculation
Scleroderma renal crisis occurs in 10% of patients with systemic sclerosis carrying a poor prognosis. A kidney biopsy is consistent with thrombotic microangiopathy (TMA) with clinical findings discerning it from other TMAs. Progression to ESRD occurs in 50% of patients which can lead to further complications necessitating emergent interventions including dialysis. Patients with scleroderma can have pericardial involvement with tamponade physiology requiring intervention such as pericardiocentesis.