Open AccessA young woman with steroid‐responsive, IgG4‐positive plasma cell‐enriched cystic lymphangioma and chylous ascites
Author(s) -
Al Zaki Alaa A.,
Mann Shawna L.,
Carruthers Mollie N.,
Slack Graham W.,
Chen Luke Y. C.
Publication year - 2018
Publication title -
clinical case reports
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.21
H-Index - 9
ISSN - 2050-0904
DOI - 10.1002/ccr3.1536
Subject(s) - medicine , lymphangioma , lymphatic system , chylous ascites , chyle , pathology , plasma cell , complication , bone marrow
Key Clinical Message Lymphangiomas are benign tumors of the lymphatic vessels, which can be inflammatory and occasionally steroid‐responsive. IgG4‐related disease (IgG4‐ RD ) is a recently defined fibro‐inflammatory condition. We describe a novel association between reactive IgG4+ plasma cells and cystic lymphangioma in a young woman who had a dramatic clinical response to steroids.