Open AccessStepwise management of hepatocellular carcinoma associated with Abernethy syndrome
Author(s) -
Christou Niki,
Dib Nabil,
Chuffart Etienne,
Taibi Abdelkader,
DurandFontanier Sylvaine,
Valleix Denis,
Mathonnet Muriel
Publication year - 2018
Publication title -
clinical case reports
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.21
H-Index - 9
ISSN - 2050-0904
DOI - 10.1002/ccr3.1384
Subject(s) - medicine , hepatocellular carcinoma , hepatoblastoma , liver transplantation , embolization , arterial embolization , portal vein , hepatectomy , radiology , resection , surgery , transplantation
Key Clinical Message Patients with congenital agenesis of the portal vein may develop hepatocellular tumors due to enhanced arterial blood flow. These tumors may be benign (FNH, adenomas) or malignant (hepatoblastoma, HCC). Liver resection can be proposed, and preoperative arterial embolization may decrease blood loss during surgery. Liver transplantation with PV reconstruction is also an option.