Open AccessErdheim‐Chester Disease with atrial mass and perinephric calcification
Author(s) -
VillatoroVillar Michel,
Koster Matthew J.
Publication year - 2017
Publication title -
clinical case reports
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.21
H-Index - 9
ISSN - 2050-0904
DOI - 10.1002/ccr3.1258
Subject(s) - medicine , erdheim–chester disease , calcification , retroperitoneal fibrosis , asymptomatic , pathology , infiltration (hvac) , fibrosis , histiocyte , histiocytosis , disease , radiology , physics , thermodynamics
Key Clinical Message Erdheim‐Chester Disease is a multi‐systemic condition characterized by non‐Langerhans histiocytic infiltration. Cardiovascular involvement with pseudotumoral infiltration of the right atrium is present in approximately one‐third of patients and may be asymptomatic. Although retroperitoneal fibrosis is common, perinephric dystrophic calcification has not been previously described.