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Percutaneous device closure of abernethy malformation—A treatable cause of hepatopulmonary syndrome
Author(s) -
Venkateshwaran Subramanian,
Krishnamoorthy Kavassery Mahadevan,
Sivasankaran Sivasubramonian
Publication year - 2013
Publication title -
catheterization and cardiovascular interventions
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.988
H-Index - 116
eISSN - 1522-726X
pISSN - 1522-1946
DOI - 10.1002/ccd.25275
Subject(s) - medicine , hepatopulmonary syndrome , percutaneous , surgery , radiology , liver transplantation , transplantation
An eight‐year‐old girl was evaluated for unexplained cyanosis. A contrast echo was suggestive of pulmonary arteriovenous fistula. Further evaluation revealed Abernethy malformation (type 2) leading to hepatopulmonary syndrome. Percutaneous device closure of Abernethy malformation was done after anatomical and physiological evaluation of the portal circulation. Prior to closure, it is important to ensure adequate portal radicals into the liver and normal portal pressure after test balloon occlusion. Subcostal echocardiography can diagnose and guide device closure of Abernethy malformation, a treatable cause of hepatopulmonary syndrome. © 2013 Wiley Periodicals, Inc.