Premium
Ectopia cordis: A rare congenital anomaly
Author(s) -
Gabriel Abigail,
Donnelly Joseph,
Kuc Alexander,
Good Daniel,
Doros Gabriela,
Matusz Petru,
loukas marios
Publication year - 2014
Publication title -
clinical anatomy
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.667
H-Index - 71
eISSN - 1098-2353
pISSN - 0897-3806
DOI - 10.1002/ca.22402
Subject(s) - medicine , presentation (obstetrics) , etiology , sternum , anatomy , thoracic cavity , anomaly (physics) , radiology , physics , condensed matter physics
Ectopia cordis (EC) is a rare congenital anomaly associated with the heart positioned outside of the thoracic cavity either partially or completely. The ectopic heart can be found along a spectrum of anatomical locations, including the cervical, thoracic and abdominal regions and in most cases, it protrudes outside the chest through a split sternum. Although the first case of EC was identified during the early 1600s only 91 cases have been reported since then in the literature. This review will discuss the history and prevalence of EC, its etiology, morphology, presentation and symptoms, complications, diagnosis, treatment and management and prognosis. Clin. Anat. 27:1193–1199, 2014. © 2014 Wiley Periodicals, Inc.