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Nomenclature of Cutaneous Vasculitis
Author(s) -
Sunderkötter Cord H.,
Zelger Bernhard,
Chen KoRon,
Requena Luis,
Piette Warren,
Carlson J. Andrew,
Dutz Jan,
Lamprecht Peter,
Mahr Alfred,
Aberer Elisabeth,
Werth Victoria P.,
Wetter David A.,
Kawana Seiji,
Luqmani Raashid,
Frances Camille,
Jorizzo Joseph,
Watts J. Richard,
Metze Dieter,
Caproni Marzia,
Alpsoy Erkan,
Callen Jeffrey P.,
Fiorentino David,
Merkel Peter A.,
Falk Ronald J.,
Jennette J. Charles
Publication year - 2018
Publication title -
arthritis and rheumatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 4.106
H-Index - 314
eISSN - 2326-5205
pISSN - 2326-5191
DOI - 10.1002/art.40375
Subject(s) - nomenclature , cutaneous vasculitis , vasculitis , dermatology , medicine , pathology , biology , zoology , taxonomy (biology) , disease
Objective To prepare a dermatologic addendum to the 2012 revised International Chapel Hill Consensus Conference Nomenclature of Vasculitides ( CHCC 2012) to address vasculitides affecting the skin (D‐ CHCC ). The goal was to standardize the names and definitions for cutaneous vasculitis. Methods A nominal group technique with a facilitator was used to reach consensus on the D‐ CHCC nomenclature, using multiple face‐to‐face meetings, e‐mail discussions, and teleconferences. Results Standardized names, definitions, and descriptions were adopted for cutaneous components of systemic vasculitides (e.g., cutaneous IgA vasculitis as a component of systemic IgA vasculitis), skin‐limited variants of systemic vasculitides (e.g., skin‐limited IgA vasculitis, drug‐induced skin‐limited antineutrophil cytoplasmic antibody–associated vasculitis), and cutaneous single‐organ vasculitides that have no systemic counterparts (e.g., nodular vasculitis). Cutaneous vasculitides that were not included in the CHCC 2012 nomenclature were introduced. Conclusion Standardized names and definitions are a prerequisite for developing validated classification and diagnostic criteria for cutaneous vasculitis. Accurate identification of specifically defined variants of systemic and skin‐limited vasculitides requires knowledgeable integration of data from clinical, laboratory, and pathologic studies. This proposed nomenclature of vasculitides affecting the skin, the D‐ CHCC , provides a standard framework both for clinicians and for investigators.