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Myoclonus in adult Huntington's disease
Author(s) -
Vogel Caryn M.,
Drury Ivo,
Terry L. Cass,
Young Anne B.
Publication year - 1991
Publication title -
annals of neurology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 4.764
H-Index - 296
eISSN - 1531-8249
pISSN - 0364-5134
DOI - 10.1002/ana.410290217
Subject(s) - myoclonus , valproic acid , huntington's disease , disease , medicine , degenerative disease , pediatrics , psychology , psychiatry , epilepsy
Two brothers with clinically definite adult Huntington's disease developed disabling myoclonus years after the first signs of the disease. Their electroencephalograms were consistent with a primary generalized epilipsy, although neither man had seizures. The myoclonus was controlled with valproic acid therapy.