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Hereditary long Q‐T syndrome presenting as epilepsy: Electroencephalography laboratory diagnosis
Author(s) -
Gospe Sidney M.,
Choy Michael
Publication year - 1989
Publication title -
annals of neurology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 4.764
H-Index - 296
eISSN - 1531-8249
pISSN - 0364-5134
DOI - 10.1002/ana.410250518
Subject(s) - electroencephalography , medicine , epilepsy , abnormality , sudden death , cardiology , electrocardiography , pediatrics , psychiatry
Patients with hereditary Q‐T interval prolongation can present with seizures, syncope, and sudden death. In 2 siblings with autosomal dominant familial long Q‐T syndrome, electroencephalographic examinations performed 6 and 2 years before diagnosis included electrocardiographic tracings documenting the cardiac abnormality. A timely diagnosis of this condition may have prevented the death of 1 of these patients. Measurement of the corrected Q‐T interval on electrocardiographic tracings obtained in the electroencephalography laboratory should be considered in selected patients.