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Hearing loss in myotonic dystrophy
Author(s) -
Wright Robert B.,
Glantz Russell H.,
Butcher Jaynee
Publication year - 1988
Publication title -
annals of neurology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 4.764
H-Index - 296
eISSN - 1531-8249
pISSN - 0364-5134
DOI - 10.1002/ana.410230217
Subject(s) - myotonic dystrophy , hearing loss , audiology , medicine , sensorineural hearing loss , myotonia , pathophysiology , audiometry , pediatrics
Seventeen of 25 patients with myotonic dystrophy had moderate to severe hearing loss, usually sensorineural, that was identified by routine audiometric screening and was treatable in some patients. Further testing failed to reveal a single pathophysiological process.