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Abnormal auditory evoked potentials in hereditary motor‐sensory neuropathy
Author(s) -
SatyaMurti Saty,
Cacace Anthony T.,
Hanson Peggy A.
Publication year - 1979
Publication title -
annals of neurology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 4.764
H-Index - 296
eISSN - 1531-8249
pISSN - 0364-5134
DOI - 10.1002/ana.410050506
Subject(s) - auditory neuropathy , brainstem , sensory system , audiology , peripheral , peripheral neuropathy , medicine , hearing loss , hereditary motor and sensory neuropathy , neuroscience , psychology , pathology , disease , diabetes mellitus , endocrinology
From a kinship with a dominantly inherited motor‐sensory neuropathy, we studied 2 brothers with brainstem auditory evoked potentials and behavioral audiometric tests. They had abnormal prolongation of I‐III interpeak intervals. Wave V was poorly developed. Conventional audiometric tests did not reveal a peripheral hearing loss. It is probable that their auditory nerves and spiral ganglia are undergoing a pathophysiological process analogous to that of their peripheral nerves.